THE PRESENT-DAY VIEW ON THE PATHOGENESIS AND PREVENTION OF LIFE-THREATENING COMPLICATIONS OF PREGNANCY AND DELIVERY IN PATIENTS WITH MESENCHYMAL DYSPLASIAS (MARFAN SYNDROME, EHLERS-DANLOS SYNDROME, RENDU-WEBER-OSLER SYNDROME)


Дәйексөз келтіру

Толық мәтін

Ашық рұқсат Ашық рұқсат
Рұқсат жабық Рұқсат берілді
Рұқсат жабық Рұқсат ақылы немесе тек жазылушылар үшін

Аннотация

Objective. To systematize the current medical knowledge and experience in the management of pregnancy and delivery in patients with mesenchymal dysplasias (Marfan syndrome, Ehlers-Danlos syndrome, Rendu-Osler syndrome). Material and methods. The paper includes the data of foreign investigations and medical guidelines for this problem, which have been published in the past 5 years. Results. The paper describes the molecular bases of each syndrome, diagnostic criteria, and their clinical manifestations in various organs and systems: musculoskeletal and cardiovascular systems, the organ of vision, etc. Such patients during pregnancy are at extremely high risk for life-threatening complications. Conclusion. A successful outcome of pregnancy requires early diagnosis and a multidisciplinary approach throughout during pregnancy and delivery.

Толық мәтін

Рұқсат жабық

Авторлар туралы

Aleksandr Makatsariya

Email: gemostasis@mail.ru
RAS corresponding member, DM, Professor, Head of obstetrics and gynecology department, Head of hemostasis pathology laboratory, I.M. Sechenov First Moscow State Medical University. 119992, Russia, Moscow, Malaya Trubetskaya str. 8 bld. 2

Lyudmila Radetskaya

Email: udaeva@gmail.com
Candidate of Medical Science, Associate Professor, Senior Researcher, Obstetrics and Gynecology Department, I.M. Sechenov First Moscow State Medical University. 119992, Russia, Moscow, Malaya Trubetskaya str. 8 bld. 2

Әдебиет тізімі

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