N.N. Priorov Journal of Traumatology and OrthopedicsN.N. Priorov Journal of Traumatology and Orthopedics0869-86782658-6738Eco-Vector5034110.17816/vto50341Research ArticleStep-up approach for surgical treatment of the spinal canal stenosis in a patient with mucopolysaccharidosis type VI (Maroto–Lami syndrome)KolesovSergey V.<p>Dr. Sci. (Med.), Professor, traumatologist-orthopedist, Head of the Department of Spinal Pathology</p>dr-kolesov@yandex.ruPereverzevVladimir S.<p>traumatologist-orthopedist of the Department of Spinal Pathology</p>vcpereverz@gmail.comShvetsVladimir V.<p>Dr. Sci. (Med.), traumatologist-orthopedist, leading researcher of the Department of Spinal Pathology</p>vshvecv@yandex.ruKazminArkadiy I.<p>Cand. Sci. (Med.), traumatologist-orthopedist of the Department of Spinal Pathology</p>kazmin.cito@mail.ruSazhnevMaxim L.<p>Cand. Sci. (Med.), traumatologist-orthopedist of the Department of Spinal Pathology</p>mak.sajnev@yandex.ruPanteleevAndrey A.<p>traumatologist-orthopedist of the Department of Spinal Pathology</p>apanteleyev@gmail.comKruglikovIgor A.<p>anesthesiologist-resuscitator</p>igorkruglikov@yandex.ruN.N. Priorov Central Institute of Traumatology and Orthopedics271220202745101911202028012021Copyright © 2020, Eco-Vector2020<p><em>The article presents a clinical case of step-up surgical treatment of spinal canal stenosis at the craniovertebral and thoracolumbar level in a patient with mucopolysaccharidosis (MPS) type VI. The treatment method gives an opportunity to achieve a satisfactory result at the background of severe metabolic disease.</em></p>mucopolysaccharidosiscraniovertebral stenosisthoracolumbar kyphosisмукополисахаридозкраниовертебральный стенозгрудопоясничный кифоз[Whitley CB, Belani KG, Chang PN, et al. Long-term outcome of Hurler syndrome following bone marrow transplantation. 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