Russian Journal of Skin and Venereal DiseasesRussian Journal of Skin and Venereal Diseases1560-95882412-9097Eco-Vector3738410.17816/dv37384MonilethrixTikhonovskayaI Vsemen200890@yahoo.comKozlovskayaV Vviktoriakozlovskaya@yahoo.comTikhonovskayaI V-KozlovskayaV V-15102011145525421072020Copyright © 2011, Eco-Vector2011Monilethrix - rare genetic disorder of hair shaft with clinical picture of hair fragility. The disease is inherited autosome-dominantly and develops as a result of disorder of keratin synthesis. Review of thw literature and case report are presented.monilethrixhair fragilityмонилетриксломкость волос[Рук А., Даубер Р. Болезни волос и волосистой части головы / Под ред. Ю. К. Скрипкина. - М.: Медицина; 1985.][Dermatology / Bolognia J., Jorizzo J., Rapini R. P. et al. - St. Louis: Mosby; 2003.][Celep F., Uzumcu A., Sonmez F. M. et al. // Genet. Couns. - 2009. - Vol. 20, N 1. - P. 1-8.][Hamm H., Echternacht-Happle K., Happle R. // Z. Hautkr. - 1984. - Bd. 59, N 17. - S. 1177-1178.][Karaman G. G., Sendur N., Basar H. et al. // Eur. Acad. Dermatol. Venereol. - 2001. - Vol. 15. - P. 357-377.][Karincaoglu Y., Coskun B. K., Seyhan M. E. et al. // Am. J. Clin. Dermatol. - 2005. - Vol. 6, N 6. - P. 407-410.][Liu C. I., Hsu C. H. // Br. J. Dermatol. - 2008. - Vol. 159, N 3. - P. 741-743.][Rakowska A., Slowinska M., Czuwara J. et al. // J. Drugs Dermatol. - 2007. - Vol. 6, N 2. - P. 222-224.][Rudnicka L., Olszewska M., Rakowska A. et al. // J. Drugs Dermatol. - 2008. - Vol. 7, N 7. - P. 651-654.][Sfaello Z., Hariga J. // Arch. Belg. Dermatol. Syphiligr. - 1967. - Vol. 23, N 4. - P. 363-371.][Shalita A. R., Norris D. A. Hair and Scalp Diseases. - New York: Informa Healthcare USA, Inc.; 2008.][Smith W. G. // Br. Med. J. - 1879. - Vol. 2. - P. 291-296.][Soukup F., Burger L. // Cesk. Oftalmol. - 1963. - Vol. 19. - P. 329-332.][Sprecher E. // Clin. Dermatol. - 2005. - Vol. 23. - P. 47-55.][Stratigos A. J., Baden H. P. // Arch. Dermatol. - 2001. - Vol. 137. - P. 1465-1471.][Tomkinson J. G. // Br. Med. J. - 1932. - Vol. 2. - P. 1009- 1020.][Wallace M. P., de Berker D. A. // Clin. Exp. Dermatol. - 2010. - Vol. 35, N 1. - P. 41-46.][Wollina U., Elsner P. // Pediatr. Dermatol. - 1999. - Vol. 16, N 4. - P. 297-300.][Zheltakov M. M., Vinokurov I. N. // Vestn. Dermatol. Venerol. - 1965. - Vol. 39, N 12. - P. 58-62.][Zlotogorski A., Marek D., Horev L. et al. // J. Invest. Dermatol. - 2006. - Vol. 126, N 6. - P. 1292-1296.]