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<article xmlns:mml="http://www.w3.org/1998/Math/MathML" xmlns:xlink="http://www.w3.org/1999/xlink" xmlns:xsi="http://www.w3.org/2001/XMLSchema-instance" xmlns:ali="http://www.niso.org/schemas/ali/1.0/" article-type="other" dtd-version="1.2" xml:lang="en"><front><journal-meta><journal-id journal-id-type="publisher-id">Pharmateca</journal-id><journal-title-group><journal-title xml:lang="en">Pharmateca</journal-title><trans-title-group xml:lang="ru"><trans-title>Фарматека</trans-title></trans-title-group></journal-title-group><issn publication-format="print">2073-4034</issn><issn publication-format="electronic">2414-9128</issn><publisher><publisher-name xml:lang="en">Bionika Media</publisher-name></publisher></journal-meta><article-meta><article-id pub-id-type="publisher-id">278138</article-id><article-categories><subj-group subj-group-type="toc-heading" xml:lang="en"><subject>Articles</subject></subj-group><subj-group subj-group-type="toc-heading" xml:lang="ru"><subject>Статьи</subject></subj-group><subj-group subj-group-type="article-type"><subject></subject></subj-group></article-categories><title-group><article-title xml:lang="en">Idiopathic interstitial pneumonia: peculiarities of clinical picture and treatment</article-title><trans-title-group xml:lang="ru"><trans-title>ИДИОПАТИЧЕСКИЕ ИНТЕРСТИЦИАЛЬНЫЕ ПНЕВМОНИИ: ОСОБЕННОСТИ КЛИНИЧЕСКОЙ КАРТИНЫ И ЛЕЧЕНИЯ</trans-title></trans-title-group></title-group><contrib-group><contrib contrib-type="author"><name-alternatives><name xml:lang="en"><surname>Avdeev</surname><given-names>S N</given-names></name><name xml:lang="ru"><surname>Авдеев</surname><given-names>С Н</given-names></name></name-alternatives><bio xml:lang="ru"><p>ФГУ НИИ пульмонологии ФМБА России, Москва</p></bio><xref ref-type="aff" rid="aff1"/></contrib><contrib contrib-type="author"><name><surname>Avdeev</surname><given-names>S N</given-names></name><xref ref-type="aff" rid="aff2"/></contrib></contrib-group><aff-alternatives id="aff1"><aff><institution xml:lang="en"></institution></aff><aff><institution xml:lang="ru">ФГУ НИИ пульмонологии ФМБА России, Москва</institution></aff></aff-alternatives><aff id="aff2"><institution></institution></aff><pub-date date-type="pub" iso-8601-date="2009-10-15" publication-format="electronic"><day>15</day><month>10</month><year>2009</year></pub-date><volume>16</volume><issue>19</issue><issue-title xml:lang="en">NO19 (2009)</issue-title><issue-title xml:lang="ru">№19 (2009)</issue-title><fpage>12</fpage><lpage>19</lpage><history><date date-type="received" iso-8601-date="2023-02-23"><day>23</day><month>02</month><year>2023</year></date></history><permissions><copyright-statement xml:lang="en">Copyright ©; 2009, Bionika Media</copyright-statement><copyright-statement xml:lang="ru">Copyright ©; 2009, ООО «Бионика Медиа»</copyright-statement><copyright-year>2009</copyright-year><copyright-holder xml:lang="en">Bionika Media</copyright-holder><copyright-holder xml:lang="ru">ООО «Бионика Медиа»</copyright-holder></permissions><self-uri xlink:href="https://journals.eco-vector.com/2073-4034/article/view/278138">https://journals.eco-vector.com/2073-4034/article/view/278138</self-uri><abstract xml:lang="en"><p>Idiopathic interstitial pneumonias (IIP) combine several diseases from the group of interstitial lung disease characterized by many similar signs: unknown etiology, progressive exertional breathlessness, diffuse lesions on the lung X-ray and CT, and restrictive ventilatory insufficiency. However, these diseases have a sufficient number of differences (primarily morphological; approach to therapy and prognosis), to consider each of the forms of IIP as separate nosological entity. Modern ATS/ERS classification includes seven forms of IIP, the most common of which are discussed in this article.</p></abstract><trans-abstract xml:lang="ru"><p>Идиопатические интерстициальные пневмонии (ИИП) объединяют несколько заболеваний из группы интерстициальных заболеваний легких, характеризующихся многими сходными признаками: неизвестная этиология, прогрессирующая одышка при физических нагрузках, диффузные изменения при рентгенографии и компьютерной томографии легких, рестиктивные вентиляционные изменения. Однако эти заболевания имеют достаточное количество различий (в первую очередь морфологических; со стороны подхода к терапии и прогноза), чтобы считать каждую из форм ИИП обособленной нозологической единицей. Современная классификация ATS/ERS включает семь форм ИИП, наиболее распространенные из которых рассматриваются в настоящей статье.</p></trans-abstract><kwd-group xml:lang="en"><kwd>idiopathic pulmonary fibrosis</kwd><kwd>nonspecific interstitial pneumonia</kwd><kwd>desquamative interstitial pneumonia</kwd><kwd>cryptogenic organizing pneumonia</kwd><kwd>acute interstitial pneumonia</kwd></kwd-group><kwd-group xml:lang="ru"><kwd>идиопатический легочный фиброз</kwd><kwd>неспецифическая интерстициальная пневмония</kwd><kwd>десквамативная интерстициальная пневмония</kwd><kwd>криптогенная организующаяся пневмония</kwd><kwd>острая интерстициальная пневмония</kwd></kwd-group></article-meta></front><body></body><back><ref-list><ref id="B1"><label>1.</label><mixed-citation>American Thoracic Society/European Respiratory Society International Multidisciplinary Consensus Classification of the Idiopathic Interstitial Pneumonias. 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