GONADOBLASTOMA IN A PATIENT WITH 46,XY GONADAL DYSGENESIS


Cite item

Full Text

Open Access Open Access
Restricted Access Access granted
Restricted Access Subscription or Fee Access

Abstract

The paper describes a case of gonadoblastoma in a female patient with 46,XY (mixed) gonadal dysgenesis. The uterus, vagina, and bisexual development of external genitals were observed in the patient.

Full Text

Restricted Access

About the authors

L. V ADAMYAN

Academician V. I. Kulakov Research Center of Obstetrics, Gynecology, and Perinatology, Ministry of Health and Social Development of Russia

Email: l_adamyan@oparina4.ru

E. A KOGAN

Academician V. I. Kulakov Research Center of Obstetrics, Gynecology, and Perinatology, Ministry of Health and Social Development of Russia

Z. N MAKIYAN

Academician V. I. Kulakov Research Center of Obstetrics, Gynecology, and Perinatology, Ministry of Health and Social Development of Russia

I. A KISELEVA

Academician V. I. Kulakov Research Center of Obstetrics, Gynecology, and Perinatology, Ministry of Health and Social Development of Russia

References

  1. Адамян Л.В., Курило Л.Ф., Окулов А.Б. и др. Систематизация нозологических форм аномалий женских половых органов // Пробл. репрод. —2010. — № 3. — С. 10—14.
  2. Касаткина Э.П. Учебное пособие по дифференциальной диагностике и терапии гермафродитизма. — М.: Медицина, 1979.
  3. Кобозева Н.В., Гуркин Ю.А. Реконструктивные операции при аномалиях гениталий у девочек / Современные методы оперативного лечения в акушерстве и гинекологии. — М.: Медицина, 1983. —С. 46—50.
  4. Conn J., Gillam L., Conway G. Revealing the diagnosis of androgen insensitivity syndrome in adulthood // Br. Med. J. - 2005. — Vol. 331. — Р. 628 -630.
  5. Consortium on the Management of Disorders of Sex Differentiation. Clinical guidelines for the management of disorders of sex development in childhood // Available Accessed. — 2006. - № 5. — Р. 30.
  6. Creighton S.M. Long-term outcome of feminization surgery: the London experience // Br. J. Urol. — 2004. — Vol. 93, suppl. 3. — Р. 44 -46.
  7. Grumbach M.M., Hughes I.A., Conte F.A. Disorders of sex differentiation. In: Larsen P.R. et al. — Eds. Williams textbook of endocrinology. — 10th ed. — Heidelberg: Saunders, 2003. — Р. 842-1002.
  8. Nistal M., Gama-Fernandez E., Marino-Enriquez A. et al. Usefulness of gonadal biopsy in the diagnosis of sexual developmental disorders // Acta Urol. Esp. — 2007. — Vol. 31, № 9. — Р. 1056-1075.
  9. Lee P. A., MD, Houk C. P., Faisal Ahmed S. Consensus statement on management of intersex disorders. // Pediatrics. — 2006. — Vol. 118, № 2. — Р. e488—e500.
  10. Von Prader A. Der genital befund beim pseudoherm aproditus feminus des kongenitalen adrenogenitalen syndromes // Helv. Pediatr. Acta. — 1954. — Vol. 9. — Р. 231-248.
  11. Woods M.S., Shepard R.G., Hardman D.A., Woods H.J. Congenital genitourinary anomalies. Is the a predilection for multiple primary malignant neoplasms // Cancer. — 1992. — Vol. 69, № 2. — Р. 546—549.

Supplementary files

Supplementary Files
Action
1. JATS XML

Copyright (c) 2011 Bionika Media

This website uses cookies

You consent to our cookies if you continue to use our website.

About Cookies