Fetal diaphragmatic hernia: Diagnosis, treatment, postnatal outcomes


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Abstract

Objective. To assess the possibility of using echography in the diagnosis and prediction of postnatal outcome in congenital diaphragmatic hernia in a fetus. Material and methods. Forty-four publications of leading Russian and foreign investigators were analyzed. Results. The accuracy of intrauterine diagnosis of diaphragmatic hernias is 60-70%; the detection time varies from 24 to 26 weeks of pregnancy and depends on the site of the lesion and the presence of comorbidity. The echographic signs of this abnormality include cardiac compression and displacement, contralateral diaphragmatic defect, and the emergence of abdominal organs in the chest. In bilateral diaphragmatic defect, the liver is determined in the right chest and intestinal loops and stomach are in that in the left chest. Conclusion. The main prognostic signs that correlate with survival include comorbidity, the intrathoracic location of the liver, the degree of pulmonary hypoplasia, and cardiac compression index.

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About the authors

Natalya Valerievna Mashinets

Research Center of Obstetrics, Gynecology and Perenatology, Ministry of Health of Russia

Email: natashamashinets@yandex.ru
PhD, the senior scientific worker of the department of functional diagnostics department of diagnostic imaging

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