URODYNAMIC DISORDERS IN A PATIENT WITH SACRAL AGENESIS


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Abstract

Sacral agenesis is a rare anomaly with a frequency of up to 1:100 thousand newborns. This malformation can be either unique or combined with abnormalities of other organs and systems. With agenesis of the sacrum of types 1-3 according to T. Renshaw, a sufficiently satisfactory connection of the spine with the pelvis is revealed, which allows the patient to verticalize and move. In addition to the orthopedic component of the anomaly, in patients, violations of the function of the pelvic organs - the bladder and the evacuation function of the colon-come to the fore. The authors of the article describe a clinical observation - a 4-year-old patient, the results of a urodynamic examination against the background of therapy with a combination of M-holinoblokator and alpha-adrenoblokator. The possibilities of correcting the function of the bladder-restoration of capacity and reduction of detrusor hypertension against the background of the therapy are shown.

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About the authors

S. S Nikitin

Children’s Republican Hospital named after I.N. Grigovich; Petrozavodsk State University

Email: ssnikitin@yandex.ru
Dr.Med.Sci., professor of the department of pediatrics and pediatric surgery Petrozavodsk State University Petrozavodsk, Russia

N. B Guseva

Children’s City Clinical Hospital No. 9 named after G. N. Speransky; Institute of clinical pediatric surgery named after N. I. Pirogov; Center of Child Psychoneurology

Email: guseva-n-b@yandex.ru
Dr.Med.Sci., professor, head of the Center of Urology, Andrology and Pathology of Pelvic Organs of the Children’s City Clinical Hospital No. 9 named after G. N. Speransky, Chief Researcher of the Research Institute of Clinical Surgery of the N. I. Pirogov Russian National Research University of the Ministry of Health of the Russian Federation, Chief Researcher of the Center of Psychoneurology Moscow, Russia

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