Surgical correction of urogenital sinus in girls


Cite item

Full Text

Open Access Open Access
Restricted Access Access granted
Restricted Access Subscription or Fee Access

Abstract

Aim. To analyze the diagnostics results and surgical outcomes in girls with congenital urogenital sinus. Materials and methods. A total of 9 girls with urogenital sinus were evaluated and treated in the clinical base of the Department of Hospital Pediatric Surgery with a course of oncology at TashPMI during the period from 2009 to 2019. Results. The results of diagnostics and treatment of 9 patients with various forms of urogenital sinus are presented. In 6 cases the anterior sagittal (transanal) approach was used. The karyotype in 8 girls corresponded to 46,XX, while another girl has karyotype of 46;X0, which is typical for Turner syndrome. Severe degree of virilization was found in 2 patients, which required clitoroplasty. Conclusion. Traditional methods of surgical correction and modified procedures provide an optimal approach and facilitate the urethral dissection from the vagina with subsequent advancement to the perineum, significantly reducing the indications for the performing a preliminary colostomy.

Full Text

Restricted Access

About the authors

F. A Otamuradov

Termez branch of the Tashkent Medical Academy

Email: furkatnet@mail.ru
PhD, Director Termez, Uzbekistan

N. Sh Ergashev

Tashkent Pediatric Medical Institute

Email: nasriddin.ergashev@mail.ru
Ph.D., MD, professor, Head of the Department of Hospital Pediatric Surgery Termez, Uzbekistan

References

  1. Macedo A., Cruz M.L., Liguori R., Trivelato R., Ottoni S.L., et al. Total urogenital mobilization by CAH: A step-by-step illustration of the technique. Journal of Pediatric Urology. 2015;11:47-48.
  2. Holschneider A.M., Hutson J.M. Anorectal Malformations in Children. Embryology, diagnosis, surgical treatment, follow-up. Heidelberg: Springer, 2006. P 251.
  3. Kagantsov I.M., Shiryaev N.D., Roberto de Castro. Surgical correction of the high urogenital sinus in girls with congenital adrenal hyperplasia using the anterior sagittal transanorectal approach. Journal of Pediatric Surgery, Anesthesia and Intensive Care 2018;8(1):13-22.Russian @@Каганцов И.М., Ширяев Н.Д., Роберто де Кастро. Хирургическая коррекция высокого урогенитального синуса у девочек с врожденной гиперплазией надпочечников передним сагиттальным трансаноректальным доступом. Российский вестник детской хирургии, анестезиологии и реаниматологии. 2018:8(1):13-22.
  4. Campbell Walsh Urology 10th Edition. Wein A., Kavoussi L., Novic E., Partin A., Peters (USA (2013).
  5. Bailez M.M., Cuenca E.S., Dibenedetto V. Urinary continence following repair of ii high urogenital sinus (UGS) in CAH. Experience with 55 cases. Frontiers in Pediatrics. Pediatric Urology. 2014; 2(67):1-6.
  6. Ruggeri G., Gargano T., Antonellini C., Carlini V., Randi B., Destro F., et al. Vaginal malformations: a proposed classification based on embryological, anatomical and clinical criteria and their surgical management (an analysis of 167 cases). Pediatr Surg Int 2012;28:797-803.
  7. Marei M.M., Fares A.E., Abdelsattar A.H., Abdullateef K.S., Serif H., et al. Anatomical measurements of the urogenital sinus in virilized female children due to congenital adrenal hyperplasia. Journal of Pediatric Urology. 2016;12:282.e1-282.e8.
  8. Seranio B.S.N., Darge K., Canning D.A., Back S.J. Contrast enhanced genitosonography (CEGS) of urogenital sinus: A case of improved conspicuity with image inversion. Radiology Case Reports.2018;13:652-654.
  9. Ashour K., Shehata S., Osheba A. Cystourethroscopy versus contrast studies in urogenital sinus and cloacal anomalies in children. Journal of Pediatric Surgery. 2018;53:313-315.
  10. Jesus V.M., Buriti F., Lessa R., Toralles M.B., Oliveira L. B. Barroso U. Total urogenital sinus mobilization for ambiguous genitalia. Journal of Pediatric Surgery. 2018;53:808-812.
  11. Tugtepe H., Thomas D. T, Turan S. Does common channel length affect surgical choice in female congenital adrenal hyperplasia patients? J. Pediatric Urology. 2014;10:948-954.
  12. Gonzalez R., LudwikiwskiB. Management of the high urogenital sinus - Risk of overexposure? J. Urology. 2012;187:787-788.
  13. Lima M., Destro F., Cantone N., MohamedMahmoud AbdEl-Aleem Shalaby, Ruggeri G. Anterior Sagittal Approach and Total Urogenital Mobilization for the Treatment of Persistent Urogenital Sinus in a 2-Year-Old Girl. European Journal of Pediatric Surgery Reports. 2016;4:13-16.
  14. Morozov D.A., Ayryan E.K., Sataeva Z.F. Feminizing plastic during virilization of the external genitalia. Urology. 2019;2:108-112.Russian @@Морозов Д.А., Айрян Э.К., Сатаева З.Ф. Феминизирующая пластика при вирилизации наружных гениталий. Урология.2019.2:108-112.
  15. Rink R.C. and Cain M.P. Surgery Urogenital mobilization for urogenital sinus repair Illustrated - Surgical Atlas. Journal compilation 2008 BJU International I 102:1182-1197.
  16. Satyanarayan A., Kavoussi N.L., Carmel M.E. Congenital Duplication of the Urogenital Sinus in an Adult Female. J. Urology.2018;122:19-23.

Supplementary files

Supplementary Files
Action
1. JATS XML

This website uses cookies

You consent to our cookies if you continue to use our website.

About Cookies