Non-ischemic priapism (post-traumatic arteriovenous fistula of the right cavernous body) in the background of Landusy-Dejerine myopathy

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Abstract

Landouzy-Dejerine myopathy (Facial-shoulder-shoulder myodystrophy) is a disease which causes weakness of the muscles of the shoulder girdle, back and hip muscles, which predisposes patients to an increased risk of injury and disability. The article presents a clinical observation of non-ischemic priapism, which developed as a result of perineal trauma with the formation of a fistula of the right cavernous body in a patient against the background of facial shoulder-shoulder myodystrophy. Methods for the differential diagnosis of this condition are also discussed.

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About the authors

Sergei V. Popov

St. Luke Clinic State Budgetary Health Institution of St. Petersburg; Military Medical Academy named after S.M. Kirov

Email: doc.popov@gmail.com
ORCID iD: 0000-0003-2767-7153

Doctor of Science, professor of the department of urology of Military-medical academy named after S.M. Kirov, Head physician of Clinical Hospital of St. Luke

Russian Federation, Saint-Petersburg; St. Petersburg

Igor N. Orlov

St. Luke Clinic State Budgetary Health Institution of St. Petersburg; North-Western State Medical University named after I.I. Mechnikov

Email: doc.orlov@gmail.com
ORCID iD: 0000-0001-5566-9789

candidate of medical sciences, head of the urology department No. 1, St. Luke Clinic State Budgetary Health Institution of St. Petersburg

Russian Federation, Saint-Petersburg; Saint-Petersburg

Timur M. Topuzov

St. Luke Clinic State Budgetary Health Institution of St. Petersburg

Email: ttopuzov@gmail.com
ORCID iD: 0000-0002-5040-5546

candidate of medical sciences, head of the urology department No. 1, St. Luke Clinic State Budgetary Health Institution of St. Petersburg

Russian Federation, Saint-Petersburg

Shamil M. Asadulaev

St. Luke Clinic State Budgetary Health Institution of St. Petersburg; North-Western State Medical University named after I.I. Mechnikov

Email: asadulaev@mail.ru

candidate of medical sciences, physician of X-ray endovascular diagnosis and treatment, St. Luke Clinic State Budgetary Health Institution of St. Petersburg

Russian Federation, Saint-Petersburg; Saint-Petersburg

Stanislav G. Vintskovsky

St. Luke Clinic State Budgetary Health Institution of St. Petersburg

Email: endovaskular@mail.ru

head of the department of X-ray surgical methods of diagnosis and treatment, physician of X-ray endovascular diagnosis and treatment, St. Luke Clinic State Budgetary Health Institution of St. Petersburg

Russian Federation, Saint-Petersburg

Evgeny A. Grin

St. Luke Clinic State Budgetary Health Institution of St. Petersburg

Author for correspondence.
Email: sv.lukaendouro@gmail.com
ORCID iD: 0000-0002-8685-6525

urologist of the urology department No. 1, St. Luke Clinic State Budgetary Health Institution of St. Petersburg

Russian Federation, Saint-Petersburg

Artem R. Orlov

Pavlov First State Medical University of St. Petersburg

Email: aorlov.9919@gmail.com

student, Pavlov First State Medical University of St. Petersburg

Russian Federation, Saint-Petersburg

Mikhail A. Kotlov

North-Western State Medical University named after I.I. Mechnikov

Email: kotlovm2013@yandex.ru
ORCID iD: 0000-0001-5336-8245

student, North-Western State Medical University named after I.I. Mechnikov

Russian Federation, Saint-Petersburg

Nikita I. Dub

Military Medical Academy named after S.M. Kirov

Email: abarmotkot98@gmail.com

student, Military Medical Academy named after S.M. Kirov

Russian Federation, St. Petersburg

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Supplementary files

Supplementary Files
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2. Fig. 1. Appearance of the patient with facial-scapulohumeral myodystrophy. Own observation

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3. Fig. 2. Arteriovenous fistula of the right corpus cavernosum during Dopplerography of the penis

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4. Fig. 3. Area of extravasation in the projection of the proximal part of the penis during selective angiography

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5. Fig. 4. Absence of extravasation during control angiography after superselective embolization of a compromised branch of the penile artery

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