SIGMOVAGINOPLASTY IN PATIENT WITH TESTICULAR FEMINIZATION SYNDROME
- Авторлар: Komyakov B.K1, Guliyev B.G1, Onoshko M.V1
-
Мекемелер:
- Northwestern State Medical University named after I.I. Mechnikov
- Шығарылым: № 3 (2014)
- Беттер: 69-71
- Бөлім: Articles
- URL: https://journals.eco-vector.com/1728-2985/article/view/280202
- ID: 280202
Дәйексөз келтіру
Аннотация
The article presents the description of the clinical observation of the 36 years old patient with testicular feminization syndrome: genetic (karyotype 46 XY) and gonadal male sex, female external genitalia and the absence of derivatives of Mullerian ducts (uterus, fallopian tubes, the upper third of the vagina). At the first stage, testes were removed; then, vaginoplasty using segment of the sigmoid colon for possible sexual intercourse was performed. There were no complications. Currently, the patient's condition is satisfactory; she lives a regular sex life.
Толық мәтін
Авторлар туралы
B. Komyakov
Northwestern State Medical University named after I.I. MechnikovDepartment of Urology St. Petersburg
B. Guliyev
Northwestern State Medical University named after I.I. Mechnikov
Email: gulievbg@mail.ru
MD, Prof. at the Depatment St. Petersburg
M. Onoshko
Northwestern State Medical University named after I.I. MechnikovDepartment of Urology St. Petersburg
Әдебиет тізімі
- Morris J.M. The syndrome of testiculare feminization in male pseudophermadoites. Am. J. Obstet Gynecol 1953; 65: 1192-1211.
- Агаджанова Е.М., Айрапетян Э.М. Неполная форма синдрома тестикулярной феминизации. Проблемы репродукции. 2007; 5: 68-73.
- Вихляева Е.М. Руководство по эндокринной гинекологии. М., МИА, 2006. 206 с.
- Жуковский М.А., Лебедев Н.Б., Семичева Т.В. и др. Нарушения полового развития. М., Медицина, 1989. 272 с.
- Balducci R., Ghirri P., Brown T.R. et al. A clinicals looks at androgen resistance. Steroids 1996; 61: 205-211.
- Conn J., Gillam L., Conway G.S. Revealing the diagnosis of androgen insensitivity syndrome in adulthood. BMJ 2005; 331: 628-630.
- Nitsche E.M., Hiort O. The molecular basis of androgen insensitivity. Hormon. Res. 2000;54:327-333.
- Джавад-Заде М.Д.,Гусейнов Э.Я.,Гусейнова Т.Т.,Магеррамов А.Д. Коррекция пола при синдроме тестикулярной феминизации. Урология. 2003;1:52-55.
- Уиллис К.Р. Атлас оперативной гинекологии. М.: Медицинская литература, 2007. 320 с.
- Moriya K., Mitsui T., Tanaka H. et al. A case of laparoscopic assisted sigmoid colon vaginoplasty for 46 XY patient with lipoid congenital adrenal hyperplasia. 29 th Congress of World Society of Endourology and SWL. Abstracts. Kuoto, 2011. A. 324.