EOSINOPHILIC GRANULOMATOSIS WITH POLYANGIITIS (CHURG-STRAUSS SYNDROME) IN A FEMALE PATENT WITH INHERTED HYPERTROPHIC CARDIOMYOPATHY


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Abstract

The paper describes a clinical case in a young female patient with eosinophilic granulomatosis with polyangiitis (EGPA) involving the gastrointestinal tract, peripheral nervous system, and lung, as well as hypertrophic cardiomyopathy. The case demonstrates differential diagnostic difficulties in patients with cardiac lesion in EGPA. The data available in the Russian and foreign literature on heart disease in patients with EGPA are analyzed.

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About the authors

L. Strizhakov

I.M. Sechenov First Moscow State Medical University

Email: strizhakov76@mail.ru
Professor

P. Novikov

I.M. Sechenov First Moscow State Medical University; University Clinical Hospital Three, I.M. Sechenov First Moscow State Medical University

E. Zhabina

I.M. Sechenov First Moscow State Medical University

T. Shevtsova

I.M. Sechenov First Moscow State Medical University

S. Moiseev

I.M. Sechenov First Moscow State Medical University

Professor

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