A case of fulminant ANCA-negative Wegener’s granulomatosis with primary ENT involvement


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Abstract

The paper describes a rare case of ANCA-negative Wegener's granulomatosis with a severe, fulminant course, which is manifested by primary ENT involvement.

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About the authors

D. Fernando

Aleksandro-Mariinsk Regional Clinical Hospital; Astrakhan State Medical University; Astrakhan Branch, Otorhinolaryngology Research and Clinical Center, Federal Biomedical Agency of Russia

Email: dinafernando.lor@gmail.com
Candidate of Medical Sciences

V. Shpotin

Aleksandro-Mariinsk Regional Clinical Hospital; Astrakhan State Medical University; Astrakhan Branch, Otorhinolaryngology Research and Clinical Center, Federal Biomedical Agency of Russia

A. Gostyunin

Aleksandro-Mariinsk Regional Clinical Hospital

S. Kudaev

Postmortem Examination Bureau

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