Current aspects of the management of patients with idiopathic pulmonary arterial hypertension

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Abstract

A clinical case of a young patient with idiopathic pulmonary arterial hypertension (iPAH) is reviewed, showing the importance of timely escalation and modification of treatment tactics after each functional status assessment. The main goal of PAH therapy is to maintain a low-risk profile. Modern approaches to PAH therapy are based on a regular comprehensive assessment of the risk of mortality and disease progression in order to carry out timely escalation. Early administration of double/triple combination therapy is the key to improving the prognosis in patients with PAH. It is especially important to consider choosing a drug with a proven effect on the long-term prognosis, which can improve the treatment results of patients with PAH.

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About the authors

L. D. Khidirova

Novosibirsk State Medical University, Ministry of Health of Russia; Novosibirsk Regional Clinical Cardiological Dispensary

Author for correspondence.
Email: h_ludmila73@mail.ru
ORCID iD: 0000-0002-1250-8798

Doctor of Medical Sciences, Professor

Russian Federation, Novosibirsk; Novosibirsk

V. N. Tyupina

Novosibirsk Regional Clinical Cardiological Dispensary

Email: h_ludmila73@mail.ru
Russian Federation, Novosibirsk

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