Clinical variants of respiratory dysfunction in children with Fontan hemodynamic

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详细

Children who born with a functional single ventricle undergo a series of surgical interventions at an early age, leading to the formation of Fontan circulation. Fontan circulation can lead to various disorders of pulmonary blood flow, depending on the specific heart defect, the volume of surgical interventions, the development of complications in the postoperative period, etc. Fontan circulation during the first years of life can lead to significant changes in pulmonary blood flow, which can affect long-term lung function. Also, functional changes in the lungs can also cause persistent circulatory disorders. Understanding the cardiopulmonary interactions along with improved recognition and treatment of pulmonary abnormalities may improve the long-term outcomes in this patient population.

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作者简介

A. Shudueva

N.I. Pirogov Russian National Research Medical University, Ministry of Health of Russia

编辑信件的主要联系方式.
Email: yulmiz@mail.ru
ORCID iD: 0000-0002-6956-1418
俄罗斯联邦, Moscow

I. Kovalev

A.N. Bakulev National Medical Research Center for Cardiovascular Surgery, Ministry of Health of Russia

Email: yulmiz@mail.ru
ORCID iD: 0000-0001-8195-5682
SPIN 代码: 5024-6323

Professor, MD

俄罗斯联邦, Moscow

Yu. Mizernitskiy

N.I. Pirogov Russian National Research Medical University, Ministry of Health of Russia

Email: yulmiz@mail.ru
ORCID iD: 0000-0002-0740-1718
SPIN 代码: 6135-5260

Professor, MD

俄罗斯联邦, Moscow

参考

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2. Fig. 1. Fontan hemodynamics (description in text)

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3. Fig. 2. Perfusion pneumoscintigraphy of girl A. demonstrates a marked impairment of perfusion of the right lung

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4. Fig. 3. Perfusion pneumoscintigraphy of girl S. demonstrates impaired perfusion of the right lung

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