PREGNANCY-ASSOCIATED ATYPICAL HEMOLYTIC-UREMIC SYNDROME: TREATMENT FEATURES, DIAGNOSTIC DIFFICULTIES, THERAPEUTIC APPROACHES


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Abstract

The paper describes pregnancy-associated atypical hemolytic-uremic syndrome (aHUS), a rare case in the clinical practice of a nephrologist. Our demonstrated case illustrates diagnostic difficulties, the specif ic features of clinical manifestations and course of obstetric aHUS, and the possibilities of a good outcome of this severe life-threatening disease for the mother and fetus provided that its diagnosis is timely established and effective plasmapheresis carried out.

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About the authors

T. V KIRSANOVA

Academician V.I. Kulakov Research Center of Obstetrics, Gynecology, and Perinatology, Ministry of Health of Russia

L. I MERKUSHEVA

Academician V.I. Kulakov Research Center of Obstetrics, Gynecology, and Perinatology, Ministry of Health of Russia; I.M. Sechenov First Moscow State Medical University

Department of Nephrology and Hemodialysis, Faculty for Postgraduate Training of Physicians

N. L KOZLOVSKAYA

I.M. Sechenov First Moscow State Medical University

Department of Nephrology and Hemodialysis, Faculty for Postgraduate Training of Physicians

T. A FEDOROVA

Academician V.I. Kulakov Research Center of Obstetrics, Gynecology, and Perinatology, Ministry of Health of Russia

Email: tfedorova1@mail.ru

N. K RUNIKHINA

Academician V.I. Kulakov Research Center of Obstetrics, Gynecology, and Perinatology, Ministry of Health of Russia

Email: runishi@rambler.ru

N. E KAN

Academician V.I. Kulakov Research Center of Obstetrics, Gynecology, and Perinatology, Ministry of Health of Russia

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