Obstructed hemivagina (OHVIRA syndrome) or uterovaginal septum and ipsilateral renal anomaly?

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Abstract

This review analyzes an update on the clinical presentations of female genitourinary malformations (OHVIRA or Herlyn-Werner-Wunderlich syndrome) and new approaches to their diagnosis and treatment. The review includes data from foreign and Russian articles found in PubMed on the topic under consideration and published in recent years. The state-of-the-art in the area under study is analyzed. The data on the diagnosis and management of patients with the rare associative state are systematized; further areas that require in-depth study are identified. Conclusion: The presented studies indicate that there is a need to revise the name of the Herlyn-Werner- Wunderlich syndrome and the acronym OHVIRA in favor of uterovaginal septum and ipsilateral renal anomaly. The important role of and need for the widespread introduction of visual diagnostic methods and minimally invasive surgical treatment technologies in the management of these patients in order to improve the efficiency of medical care are emphasized.

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About the authors

Zalina K. Batyrova

Academician V.I. Kulakov National Medical Research Center of Obstetrics, Gynecology, and Perinatology, Ministry of Health of Russia

Email: linadoctor@mail.ru
PhD, Senior Researcher at the Department of Pediatric and Adolescent Gynecology

Elena V. Uvarova

Academician V.I. Kulakov National Medical Research Center of Obstetrics, Gynecology, and Perinatology, Ministry of Health of Russia; I.M. Sechenov First Moscow State Medical University (Sechenov University), Ministry of Health of Russia

Email: elena-uvarova@yandex.ru
Corresponding member of the RAS, Dr. Med. Sci., Professor, Head of the Department of Pediatric and Adolescent Gynecology; Professor at the Department of Obstetrics, Gynecology, Perinatology and Reproductology, President of Interregional Public Organization "Association of Pediatric and Adolescent Gynecologists”

Vladimir D. Chuprynin

Academician V.I. Kulakov National Medical Research Center of Obstetrics, Gynecology, and Perinatology, Ministry of Health of Russia

Email: v_chuprynin@oparina4.ru
PhD, Head of the Surgical Department

Aleksandra V. Asaturova

Academician V.I. Kulakov National Medical Research Center of Obstetrics, Gynecology, and Perinatology, Ministry of Health of Russia

Email: a.asaturova@gmail.com
PhD, Head of the Department of Anatomic Pathology

Zaira Kh. Kumykova

Academician V.I. Kulakov National Medical Research Center of Obstetrics, Gynecology, and Perinatology, Ministry of Health of Russia

Email: zai-kumykova@yandex.ru
PhD, Senior Researcher at the Department of Pediatric and Adolescent Gynecology

Diana A. Kruglyak

Academician V.I. Kulakov National Medical Research Center of Obstetrics, Gynecology, and Perinatology, Ministry of Health of Russia

Email: diana.kruglyak@yandex.ru
doctor at the Department of Pediatric and Adolescent Gynecology

Marina S. Gautier

National Medical Research Center for Children's Health, Ministry of Health of Russia

Email: marina.gautier@gmail.com
Pediatrician, Department of Rheumatology

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