Use of an ex utero intrapartum treatment procedure in a fetus with prenatally diagnosed neck teratoma


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Abstract

Background. The neck is the second most common site for fetal teratomas after the sacrococcygeal region. In cases of airway obstruction, neck teratomas have a poor prognosis for life. Ex utero intrapartum treatment (EXIT) can lower neonatal mortality with a multidisciplinary approach and an oxygenation procedure for the newborn with persistent utero-fetal circulation. Case report. The paper describes a clinical case of fetal neck teratoma diagnosed at 32 weeks’ gestation and complicated by bilateral hydrothorax and polyhydramnios. Fetal magnetic resonance imaging (MRI) was performed after repeated therapeutic amniodrainage, which established changes in the anatomy of the airway with tracheal displacement and compression. The trachea was laterally displaced and only partially tracked. EXIT was recommended. An EXIT procedure with bronchoscopy was done at 35 weeks’ gestation. A live boy was born, who weighed 2660 g and had an Apgar score of 6/mechanical ventilation. Surgical removal of the teratoma was successfully performed in the baby at the age of 9 days. Conclusion. When a neck tumor is prenatally detected, additional MRI is needed to determine the degree of airway displacement and/or obstruction and to schedule delivery, by attracting specialists rendering newborn care.

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About the authors

Oksana V. Pribushenya

Republican Research and Practical Center "Mother and Child", Ministry of Health of the Republic of Belarus

Email: pribushenya@yandex.ru
MD, PhD, head of the Scientific Laboratory for Medical Genetics, Republic Scientific and Practical Center „Mather and child”, professor of the department of obstetrics, gynecology and reproductive health “BelMAPE”.

Olga A. Tarletskaya

Republican Research and Practical Center "Mother and Child", Ministry of Health of the Republic of Belarus

doctor of ultrasound diagnostics of the department of prenatal diagnostics

Olga A. Pankratova

Republican Research and Practical Center "Mother and Child", Ministry of Health of the Republic of Belarus

MD, PhD, Head of the Department of Pregnancy Pathology No. 2

Dmitry B. Drozdovsky

Republican Research and Practical Center "Mother and Child", Ministry of Health of the Republic of Belarus

intensive care physician of the neonatal intensive care unit

Natalia N. Medvedeva

Clinical Maternity Hospital in the Minsk Region

obstetrician-gynecologist of the admission department

Nadezhda V. Petrovskaya

Mogilev Regional Diagnostic and Treatment Center

obstetrician-gynecologist of the Department of Medical Genetics

References

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