PREGNANCY-ASSOCIATED ATYPICAL HEMOLYTIC-UREMIC SYNDROME: TREATMENT FEATURES, DIAGNOSTIC DIFFICULTIES, THERAPEUTIC APPROACHES


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The paper describes pregnancy-associated atypical hemolytic-uremic syndrome (aHUS), a rare case in the clinical practice of a nephrologist. Our demonstrated case illustrates diagnostic difficulties, the specif ic features of clinical manifestations and course of obstetric aHUS, and the possibilities of a good outcome of this severe life-threatening disease for the mother and fetus provided that its diagnosis is timely established and effective plasmapheresis carried out.

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作者简介

T. KIRSANOVA

Academician V.I. Kulakov Research Center of Obstetrics, Gynecology, and Perinatology, Ministry of Health of Russia

L. MERKUSHEVA

Academician V.I. Kulakov Research Center of Obstetrics, Gynecology, and Perinatology, Ministry of Health of Russia; I.M. Sechenov First Moscow State Medical University

Department of Nephrology and Hemodialysis, Faculty for Postgraduate Training of Physicians

N. KOZLOVSKAYA

I.M. Sechenov First Moscow State Medical University

Department of Nephrology and Hemodialysis, Faculty for Postgraduate Training of Physicians

T. FEDOROVA

Academician V.I. Kulakov Research Center of Obstetrics, Gynecology, and Perinatology, Ministry of Health of Russia

Email: tfedorova1@mail.ru

N. RUNIKHINA

Academician V.I. Kulakov Research Center of Obstetrics, Gynecology, and Perinatology, Ministry of Health of Russia

Email: runishi@rambler.ru

N. KAN

Academician V.I. Kulakov Research Center of Obstetrics, Gynecology, and Perinatology, Ministry of Health of Russia

参考

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