The features of the course of pregnancy and the outcomes of labor during cystinuria


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Background. Cystinuria is an autosomal recessive hereditary disease associated with impaired transport of dibasic amino acids (including cystine) and with the formation of coral renal calculi, which is accompanied by frequent surgical interventions and recurrent pyelonephritis. Case report. A primigravida patient was hospitalized for a period of29-30 weeks with an exacerbation of chronic pyelonephritis of only one right working kidney. Combination treatment made it possible to prolong pregnancy up to 34 weeks. Early delivery is due to signs of renal failure. Conclusion. Strict adherence to the rules of management of pregnant women with only one working kidney in the presence of chronic pyelonephritis could delay delivery to an optimal period in terms of minimizing perinatal complications.

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作者简介

Alexander Strizhakov

I.M. Sechenov First Moscow State Medical University of the Ministry of Health of the Russian Federation (Sechenov University)

Email: kafedra-agp@mail.ru
MD, academician of the Russian Academy of Sciences, professor, head of the Department of Obstetrics, Gynecology and Perinatology of the Faculty of Medicine

Irina Bogomazova

I.M. Sechenov First Moscow State Medical University of the Ministry of Health of the Russian Federation (Sechenov University)

Email: kafedra-agp@mail.ru
PhD, associate Professor of the Department of Obstetrics, Gynecology and Perinatology of the Faculty of Medicine

Irina Ignatko

I.M. Sechenov First Moscow State Medical University of the Ministry of Health of the Russian Federation (Sechenov University)

Email: iradocent@mail.ru
MD, corresponding member of the Russian Academy of Sciences, professor of the Russian Academy of Sciences, professor of the Department of Obstetrics, Gynecology and Perinatology of the Faculty of Medicine

Vera Belousova

I.M. Sechenov First Moscow State Medical University of the Ministry of Health of the Russian Federation (Sechenov University)

Email: kafedra-agp@mail.ru
PhD, associate professor, associate professor of the Department of Obstetrics, Gynecology and Perinatology of the Faculty of Medicine

Elena Timokhina

I.M. Sechenov First Moscow State Medical University of the Ministry of Health of the Russian Federation (Sechenov University)

Email: kafedra-agp@mail.ru
MD, associate professor, professor of the Department of Obstetrics, Gynecology and Perinatology of the Faculty of Medicine

Madina Kardanova

I.M. Sechenov First Moscow State Medical University of the Ministry of Health of the Russian Federation (Sechenov University)

Email: kafedra-agp@mail.ru
PhD, assistant professor of the Department of Obstetrics, Gynecology and Perinatology of the Faculty of Medicine

Anton Kuznetsov

I.M. Sechenov First Moscow State Medical University of the Ministry of Health of the Russian Federation (Sechenov University)

Email: kafedra-agp@mail.ru
post-graduate student of the Department of Obstetrics, Gynecology and Perinatology of the Faculty of Medicine

Natalia Afanasyeva

S.S. Yudin City Clinical Hospital, Moscow Healthcare Department

Email: gkb-yudina@zdrav.mos.ru
PhD, deputy chief physician for obstetrics and gynecology

Yulia Samoilova

S.S. Yudin City Clinical Hospital, Moscow Healthcare Department

Email: gkb-yudina@zdrav.mos.ru
PhD, head of the Department of Pregnancy Pathology of maternity hospital

参考

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