Parry-Romberg progressive facial hemiatrophy

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Abstract

Parry–Romberg progressive facial hemiatrophy is an uncommon, sporadic disorder characterized by progressive hemifacial wasting and atrophy of skin, muscle, and bone, sometimes involving the central nervous system, and manifesting as focal scleroderma. Parry–Romberg syndrome, more common in women without ethnic or geographic predilections, occurs during the first or second decades of life, leading to slow and progressive facial hemiatrophy, predominantly on the left side. The diagnosis of Parry–Romberg syndrome mainly depends on clinical history using imaging studies and histopathological correlation. The article provides data on the etiology, pathogenesis, and clinical picture of the disease. Methods for diagnosing and treating these patients are described in detail.

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About the authors

Z. Sh. Garaeva

Kazan State Medical Academy (KSMA) – Branch Campus of the Russian Medical Academy of Continuous Professional Education, Department of Dermatovenereology and Cosmetology

Email: yuluizadoc@hotmail.com
ORCID iD: 0000-0001-9096-0563
SPIN-code: 3156-8170
Russian Federation, Kazan

L. A. Yusupovа

Kazan State Medical Academy (KSMA) – Branch Campus of the Russian Medical Academy of Continuous Professional Education, Department of Dermatovenereology and Cosmetology

Author for correspondence.
Email: yuluizadoc@hotmail.com
ORCID iD: 0000-0001-8937-2158
SPIN-code: 5743-6872

Dr. Sci. (Med.), Professor, Head of the Department of Dermatovenereology and Cosmetology

Russian Federation, Kazan

G. I. Mavlyutova

Kazan State Medical Academy (KSMA) – Branch Campus of the Russian Medical Academy of Continuous Professional Education, Department of Dermatovenereology and Cosmetology

Email: yuluizadoc@hotmail.com
ORCID iD: 0000-0002-4652-8869
SPIN-code: 3427-8924
Russian Federation, Kazan

E. I. Yunusovа

Kazan State Medical Academy (KSMA) – Branch Campus of the Russian Medical Academy of Continuous Professional Education, Department of Dermatovenereology and Cosmetology

Email: yuluizadoc@hotmail.com
ORCID iD: 0000-0002-4550-9578
SPIN-code: 8514-0058
Russian Federation, Kazan

A. F. Mavleeva

Kazan State Medical Academy (KSMA) – Branch Campus of the Russian Medical Academy of Continuous Professional Education, Department of Dermatovenereology and Cosmetology

Email: yuluizadoc@hotmail.com
ORCID iD: 0009-0004-4326-6025
Russian Federation, Kazan

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