Zinner syndrome in a child

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Abstract

Zinner syndrome (ZS) is a rare anomaly of the genitourinary system, characterized by a triad of symptoms: seminal vesicle cyst, ipsilateral renal aplasia, and obstruction of the vas deferens. This pathology often leads to such a complication as male infertility. The non-specificity of the symptoms dictates the difficulties in the diagnostic search and diagnosis. To date, there is no clear algorithm for managing patients with this syndrome: both conservative and surgical treatment methods can be used. The article demonstrates a clinical case of asymptomatic ZS in a 14-year-old child.

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About the authors

Sergey L. Morozov

Pirogov Russian National Research Medical University

Author for correspondence.
Email: mser@list.ru
ORCID iD: 0000-0002-0942-0103

Cand.Sci. (Med.), Leading Researcher, Department of Hereditary and Acquired Kidney Diseases named after prof. M.S. Ignatova, Research Clinical Institute of Pediatrics and Pediatric Surgery named after Acad. Yu.E. Veltischev; Associate Professor, Department of Hospital Pediatrics No. 2, Institute of Maternity and Childhood

Russian Federation, Moscow

Natalya S. Kiseleva

Pirogov Russian National Research Medical University

Email: mser@list.ru
ORCID iD: 0009-0006-0131-8899

Resident Physician at the Department of Hospital Pediatrics No. 2, Institute of Maternity and Childhood

Russian Federation, Moscow

Aleksandr R. Chizhov

Pirogov Russian National Research Medical University

Email: mser@list.ru

Resident Physician at the Department of Innovative Pediatrics and Pediatric Surgery

Russian Federation, Moscow

Lilit D. Grigoryan

Pirogov Russian National Research Medical University

Email: mser@list.ru

a pediatric surgeon, Research Clinical Institute of Pediatrics and Pediatric Surgery named after Acad. Yu.E. Veltishchev

Russian Federation, Moscow

Lyubov A. Poleshchuk

Pirogov Russian National Research Medical University

Email: mser@list.ru

Cand.Sci. (Med.), Head of the Department of Radiation Diagnostics, Research Clinical Institute of Pediatrics and Pediatric Surgery named after Acad. Yu.E. Veltishchev

Russian Federation, Moscow

Andrey N. Podgorny

Pirogov Russian National Research Medical University

Email: mser@list.ru

Cand.Sci. (Med.), Associate Professor, Surgeon, Urologist-Andrologist, Head of the Surgery Department, Scientific Research Clinical Institute of Pediatrics and Pediatric Surgery named after Acad. Yu.E. Veltishchev

Russian Federation, Moscow

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2. Fig. 1. Ultrasound image of the detected formation: visualized formation in the area of the left ureter opening

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3. Fig. 2. Urethrocystoscopy ln the projection of the left ureteral orifice, а mucosal protrusion into the lumen of the bladder is determined - indicated bу the arrow.

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4. Fig. 3. ЗА - мoment of cyst puncture, ЗВ - aspiration contents

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