Combined congenital anomaly of the bladder and urethra in a child. Possibilities of surgical treatment

Мұқаба

Дәйексөз келтіру

Толық мәтін

Ашық рұқсат Ашық рұқсат
Рұқсат жабық Рұқсат берілді
Рұқсат жабық Рұқсат ақылы немесе тек жазылушылар үшін

Аннотация

This article describes a clinical case of a combined anomaly of the urinary system in a nine-year-old boy with the presence of a posterior urethral valve and a large congenital bladder diverticulum, and also analyzes the genetic aspects of the formation of these pathologies. When examining the child, the clinical and genealogical method, functional research methods (ultrasound examination of the kidneys and bladder, intravenous urography and cystography, complex urodynamic study, cystoscopy), clinical and biochemical examination of blood and urine were used. The patient underwent transvesical diverticulum removal with bladder drainage using an indwelling Foley catheter to ensure low pressure wound healing and avoid persistent urine leakage. Treatment of children with developmental anomalies of the kidneys and urinary tract is carried out within the framework of a multidisciplinary approach with an individual management plan and constant monitoring of progressive chronic renal failure. The management strategy for patients with bladder diverticulum is based on clinical manifestations, and the decision to perform surgical treatment of children with bladder diverticulum is made by a team of specialists, which includes urologists, nephrologists, pediatric surgeons, pediatricians and functional diagnostic doctors.

Толық мәтін

Рұқсат жабық

Авторлар туралы

Sergey Morozov

Veltischev Research and Clinical Institute for Pediatrics; Pirogov Russian National Research Medical University

Хат алмасуға жауапты Автор.
Email: mser@list.ru
ORCID iD: 0000-0002-0942-0103

Cand.Sci. (Med.), Leading Researcher at the Department of Hereditary and Acquired Kidney Diseases named after. Prof. M.S. Ignatova, Veltishchev Research Clinical Institute of Pediatrics and Pediatric Surgery, Pirogov Russian National Research Medical University, Associate Professor at the Department of Hospital Pediatrics No. 2, Faculty of Pediatrics, Pirogov Russian National Research Medical University

Ресей, Moscow; Moscow

Tatyana Kursova

Veltischev Research and Clinical Institute for Pediatrics; Veltischev Research and Clinical Institute for Pediatrics

Email: kursova.tanya@yandex.ru

Laboratory Assistant-Researcher, Department of Monitoring and Information Technologies, Veltishchev Research Clinical Institute of Pediatrics and Pediatric Surgery, Department of Innovative Pediatrics and Pediatric Surgery, Faculty of Additional Professional Education

Ресей, Moscow; Moscow

Andrey Podgorny

Veltischev Research and Clinical Institute for Pediatrics

Email: mser@list.ru

Cand.Sci. (Med.), Associate Professor, Surgeon, Urologist-Andrologist, Head of the Department of Surgery

Ресей, Moscow

Lyubov Polishchuk

Veltischev Research and Clinical Institute for Pediatrics

Email: mser@list.ru

Cand.Sci. (Med.), Head of the Department of Radiation Diagnostics

Ресей, Moscow

Lilit Grigoryan

Veltischev Research and Clinical Institute for Pediatrics; Veltischev Research and Clinical Institute for Pediatrics

Email: mser@list.ru

Surgeon at the Department of Surgery, Veltishchev Research Clinical Institute of Pediatrics and Pediatric Surgery

Ресей, Moscow; Moscow

Oksana Piruzieva

Veltischev Research and Clinical Institute for Pediatrics

Email: piruzieva1987@mail.ru

Nephrologist at the Department of Hereditary and Acquired Kidney Diseases named after. prof. M.S. Ignatova

Ресей, Moscow

Evgenia Petukhova

Veltischev Research and Clinical Institute for Pediatrics

Email: evgenia99pet@gmail.com

Resident Physician at the Department of Innovative Pediatrics and Pediatric Surgery, Faculty of Additional Professional Education

Ресей, Moscow

Әдебиет тізімі

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Әрекет
1. JATS XML
2. Fig. 1. A - ultrasound of the bladder, the arrow indicates the gate of the bladder diverticulum, B - cystography, the arrow indicates the giant diverticulum of the bladder

Жүктеу (139KB)
3. Fig. 2. Clinical urodynamic study of child T.

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4. Fig. 3. Posterior urethral valve, condition after transurethral resection

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5. Fig. 4. A - neck of diverticulum, B - cavity of diverticulum

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6. Fig. 5. A - the bladder is taken on holders and opened, B - incision of the bladder mucosa in the area of ​​the diverticulum neck with mobilization and subsequent removal of the diverticulum (the diverticulum is indicated by arrows)

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