Acute disorders of cerebral circulation in persons with differentiated connective tissue dysplasias


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Abstract

Acute cerebrovascular accidents (ACVA) are common diseases in people of different sex and age. The causes of ACVA are different and deviate depending on age groups. Currently, there is an increase of stroke incidence in young patients. At a young age, ACVA can develop in persons with congenital connective tissue disorders. Such typical hereditary connective tissue diseases as Marfan syndrome, Ehlers-Danlos syndrome, Lois-Dietz syndrome and elastic pseudoxanthoma are considered thoroughly. The diagnostic criteria for these diseases, data on their prevalence and peculiarities of concomitant ACVA are presented.

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About the authors

Natalia V. Pizova

Yaroslavl State Medical University of the Ministry of Healthcare of Russia

MD, professor of the Department of nervous diseases with medical genetics and neurosurgery

Nikolay A. Pizov

Yaroslavl State Medical University of the Ministry of Healthcare of Russia

postgraduate student of the Department of nervous diseases with medical genetics and neurosurgery

Olga A. Skachkova

Yaroslavl State Medical University of the Ministry of Healthcare of Russia

postgraduate student of the Department of nervous diseases with medical genetics and neurosurgery

Vladimir A. Shadrichev

Yaroslavl State Medical University of the Ministry of Healthcare of Russia

assistant of the Department of nervous diseases with medical genetics and neurosurgery

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