Still’s disease is a great mimic of systemic inflammatory response syndrome?

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详细

Still’s disease in adults (ADS) is a rare systemic autoinflammatory disease. Fever, arthralgia, rash, and neutrophilic leukocytosis are dominating in its clinical picture. These indexes let doctors to suspect infectious diseases, sepsis and prescribe antibiotic therapy, which is ineffective. Article presents a case of a disease that debuted with high fever, shortness of breath, severe weakness and myalgia. Female patient was diagnosed according to the present symptoms, laboratory signs, taking into account the criteria of Yamaguchi M. et al. and by excluding infectious and autoimmune diseases, malignant neoplasms. Treatment with corticosteroids resulted in complete clinical remission.

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作者简介

Lyudmila Melnikova

Russian Medical Academy of Continuous Professional Education of the Ministry of Healthcare of Russia

编辑信件的主要联系方式.
Email: lumel2408@yandex.ru
ORCID iD: 0000-0003-4688-1272

MD, associate professor, professor the Department of general medical practice and polyclinic therapy, Russian Medical Academy of Continuous Professional Education of the Ministry of Healthcare of Russia

俄罗斯联邦, 125445, Moscow,19/38 Belomorskaya Str

Tatyana Lokhina

Penza Institute for Further Training of Physicians – branch of Russian Medical Academy of Continuous Professional Education of the Ministry of Healthcare of Russia

Email: ltv-13@mail.ru
ORCID iD: 0000-0002-9493-444X

MD, head of the Department of therapy, cardiology, functional diagnostics and rheumatology, Penza Institute for Further Training of Physicians – branch of Russian Medical Academy of Continuous Professional Education of the Ministry of Healthcare of Russia

俄罗斯联邦, 440060, Penza,8A Stasova Str.

Natalya Berenshtein

Penza Institute for Further Training of Physicians – branch of Russian Medical Academy of Continuous Professional Education of the Ministry of Healthcare of Russia

Email: berenshtein2011@yandex.ru
ORCID iD: 0000-0002-1589-2799

PhD in Medical Sciences, associate professor of the Department of ultrasound diagnostics, Penza Institute for Further Training of Physicians – branch of Russian Medical Academy of Continuous Professional Education of the Ministry of Healthcare of Russia

俄罗斯联邦, 440060, Penza,8A Stasova Str.

Natalya Timofeeva

G.A. Zakharyin Clinical Hospital No. 6

Email: nataliatimofeeva1805@gmail.com

deputy chief physician for medicine of G.A. Zakharyin Clinical Hospital No. 6

俄罗斯联邦, 440071, Penza,7 Stasova Str.

参考

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  9. Yamaguchi M., Ohta A., Tsunematsu T. et al. Preliminary criteria for classification of adult Still΄s disease. J Rheumatol. 1992; 19(3): 424–30.
  10. Fautrel B., Zing E., Golmard J.L. et al. Proposal for a new set of classification criteria for adult-onset Still disease. Medicine (Baltimore). 2002; 81(3): 194–200. https://dx.doi.org/10.1097/00005792-200205000-00003.

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