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Rare clinical case of the diagnosis of idiopathic pulmonary artery hypertension
- Authors: Ignatenko G.A.1, Grekov I.S.1, Grushina M.V.1, Dubovyk A.V.1
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Affiliations:
- M. Gorky Donetsk National Medical University
- Issue: Vol 29, No 2 (2021)
- Pages: 299-304
- Section: Clinical reports
- URL: https://journals.eco-vector.com/pavlovj/article/view/48940
- DOI: https://doi.org/10.17816/PAVLOVJ48940
- ID: 48940
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Abstract
In this work, a rather rare (morbidity of about 1–2 cases per 1 million of adult population per year) and interesting clinical case of the diagnosis of idiopathic pulmonary artery hypertension (IPAH) was described. This case was also known as Ayerza disease or Ayerza–Arilago syndrome. At the initial stage, this pathology was characterized by an asymptomatic course that caused certain difficulties in making a correct diagnosis. In general, this disease had a poor prognosis. The main cause of death was decompensated right ventricular failure. The occurrence of complications could be significantly reduced and the life quality of such patients could be improved by the timely diagnosis and correct approach.
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About the authors
Grigory A. Ignatenko
M. Gorky Donetsk National Medical University
Email: gai-1959@mail.ru
ORCID iD: 0000-0002-1155-563X
MD, Dr.Sci.(Med.), Professor, Corresponding Member of the Ukraine National Academy of Medical Sciences, Honored Scientist and Technician of Ukraine, Rector, Head of the Propaedeutic and Internal Medicine Department
Ukraine, DonetskIlya S. Grekov
M. Gorky Donetsk National Medical University
Email: ilya.grekov.1998@gmail.com
ORCID iD: 0000-0002-6140-5760
6th year student
Ukraine, DonetskMarina V. Grushina
M. Gorky Donetsk National Medical University
Author for correspondence.
Email: grushinamarina@inbox.ru
ORCID iD: 0000-0003-3670-3376
MD, Cand.Sci.(Med.), , Associate Professor of the Propaedeutic and Internal Medicine Department
Ukraine, DonetskAnna V. Dubovyk
M. Gorky Donetsk National Medical University
Email: dubovyk-anna@mail.ru
ORCID iD: 0000-0002-8753-3824
MD, Cand.Sci.(Med.), , Associate Professor of the Propaedeutic and Internal Medicine Department
Ukraine, DonetskReferences
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