Rare clinical case of the diagnosis of idiopathic pulmonary artery hypertension
- 作者: Ignatenko G.A.1, Grekov I.S.1, Grushina M.V.1, Dubovyk A.V.1
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隶属关系:
- M. Gorky Donetsk National Medical University
- 期: 卷 29, 编号 2 (2021)
- 页面: 299-304
- 栏目: Clinical reports
- ##submission.dateSubmitted##: 03.11.2020
- ##submission.dateAccepted##: 01.02.2021
- ##submission.datePublished##: 22.07.2021
- URL: https://journals.eco-vector.com/pavlovj/article/view/48940
- DOI: https://doi.org/10.17816/PAVLOVJ48940
- ID: 48940
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详细
In this work, a rather rare (morbidity of about 1–2 cases per 1 million of adult population per year) and interesting clinical case of the diagnosis of idiopathic pulmonary artery hypertension (IPAH) was described. This case was also known as Ayerza disease or Ayerza–Arilago syndrome. At the initial stage, this pathology was characterized by an asymptomatic course that caused certain difficulties in making a correct diagnosis. In general, this disease had a poor prognosis. The main cause of death was decompensated right ventricular failure. The occurrence of complications could be significantly reduced and the life quality of such patients could be improved by the timely diagnosis and correct approach.
全文:
作者简介
Grigory Ignatenko
M. Gorky Donetsk National Medical University
Email: gai-1959@mail.ru
ORCID iD: 0000-0002-1155-563X
MD, Dr.Sci.(Med.), Professor, Corresponding Member of the Ukraine National Academy of Medical Sciences, Honored Scientist and Technician of Ukraine, Rector, Head of the Propaedeutic and Internal Medicine Department
乌克兰, DonetskIlya Grekov
M. Gorky Donetsk National Medical University
Email: ilya.grekov.1998@gmail.com
ORCID iD: 0000-0002-6140-5760
6th year student
乌克兰, DonetskMarina Grushina
M. Gorky Donetsk National Medical University
编辑信件的主要联系方式.
Email: grushinamarina@inbox.ru
ORCID iD: 0000-0003-3670-3376
MD, Cand.Sci.(Med.), , Associate Professor of the Propaedeutic and Internal Medicine Department
乌克兰, DonetskAnna Dubovyk
M. Gorky Donetsk National Medical University
Email: dubovyk-anna@mail.ru
ORCID iD: 0000-0002-8753-3824
MD, Cand.Sci.(Med.), , Associate Professor of the Propaedeutic and Internal Medicine Department
乌克兰, Donetsk参考
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- Galiè N, Humbert M, Vachiery J-L, et al. 2015 ESC/ERS Guidelines for the diagnosis and treatment of pulmonary hypertension. European Respiratory Journal. 2015;46(4):903-75. doi: 10.1183/13993003.01032-2015
- Kochetov VE. Aerza-Arrilaga syndrome: pathogenesis and pathophysiology. Bulletin of Emergency Medicine. 2016; 9(1):107-11. (In Russ).
- Tsareva NA. Updated classification and diagnosis of pulmonary hypertension. Consilium Medicum. 2017;19(3):66-71. (In Russ).
- Martyniuk TV, Chazova IE. Strategy of medical treatment of pulmonary arterial hypertension in the current international recommendations. Systemic Hypertension. 2016;13(2):46-64. (In Russ).