Extramammary Paget’s disease
- Authors: Grekova Y.N.1, Zilberberg N.V.1, Kuznetsova E.I.2
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Affiliations:
- Ural Research Institute of Dermatovenereology and Immunopathology
- P.D. Borodin Verkhnyaya Pyshma Central Town Hospital
- Issue: No 6 (2022)
- Pages: 176-179
- Section: Articles
- URL: https://journals.eco-vector.com/0300-9092/article/view/249715
- DOI: https://doi.org/10.18565/aig.2022.6.176-179
- ID: 249715
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Abstract
Background: Extramammary Paget’s disease (EPD) is a rare tumor that most commonly affects the anogenital region. The foci often bear similarities to chronic dermatoses, which can make timely diagnosis difficult. A skin biopsy with histological and immunohistochemical studies is needed to verify the diagnosis of EPD. Most cases are treated with surgical resection, but the recurrence rate remains quite high. Case report: The paper describes a case of an EPD patient whose diagnosis was established 9 years after the onset of the disease. Conclusion: Rare localization, prolonged course, resistance to previous therapy, and pronounced subjective sensations (itching and pain) necessitate a morphopathological study.
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About the authors
Yulia N. Grekova
Ural Research Institute of Dermatovenereology and Immunopathology
Email: kjn@mail.ru
Dr. Med. Sci., Leading Researcher at the Department of Syphilidology and Sexually Transmitted Infections
Natalya V. Zilberberg
Ural Research Institute of Dermatovenereology and Immunopathology
Email: zilberberg@mail.ru
Dr. Med. Sci., Professor, Deputy Director for Research
Ekaterina I. Kuznetsova
P.D. Borodin Verkhnyaya Pyshma Central Town Hospitalgeneral practitioner
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