Clinico-morphological and electrophysiological features of neural amiotrophies

Neural amyotrophies belong to the heterogenous group of genetically determinated diseases of the nervous system. They are manifested by multiple lesions of peripheral nerves and distinguished by a heritability type, distinct clinical polymorphism, rate of symptom augmenting, peculiarities of electromyographic and morphologic changes. In accordance with Dick suggestion (1975), hereditary motosensory neuropathies were subdivided into seven types. Clinical practice shows a great variety of neural amyotrophy forms, and their quantity is likely to be well in excess of seven.