Surgical Treatment of Long Bones Deformities in Exostotic Chondrodysplasia in Children

Surgical method for the treatment of children with shin bones deformities developed on the background of multiple osteocartilagenous exostoses has been proposed. The technique consisted of exostoses removal within normal tissues, performance of osteotomy on the deformity apex, formation of autograft followed by its insertion into zone of the defect for its closure by means of fixed rate distraction and correction of limb axis in the external fixation device. That technique was applied in 11 children. Good result was achieved in 87.2%, satisfactory - in 11.5%, poor - in 1.3% of cases. In control group (24 patients treated by conventional surgical methods) good results made up 62.5%, satisfactory - 25.0%, poor - 12.5%. Closure of the defect zone by formed cortical autograft enabled to shorten the bone consolidation terms in patients who were treated by the proposed technique by 12-14 days.

children, multiple osteocartilagenous exostoses, long bone deformities, surgical treatment