Treatment of a patient with mucopolysaccharidoses type II (Hunter syndrome) complicated by craniovertebral spinal canal stenosis

Abstract


Formation of spinal canal stenosis at T12-L1 level, rarely at the level of craniovertebral junction, is a typical spinal disorder in different types of mucopolysaccharidoses that is a serious complication due to tetraparesis and tetraplegia development. Clinical, roentgenologic and therapeutic aspects of the mucopolysaccharidoses type II course in a 23 months old boy as well as the results of two-step surgical treatment for the cervical spine stabilization and elimination of spinal canal stenosis at the level of craniovertebral junction are presented.

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About the authors

Luydmila K. Mikhailova

N.N. Priorov National Medical Research Center of Traumatology and Orthopaedics

Email: cito-uchsovet1@mail.com
Moscow, Russia
Dr. med. sci., Professor, Consultant, Scientific and Outpatient department

A. A Kuleshov

N.N. Priorov National Medical Research Center of Traumatology and Orthopaedics

Moscow, Russia

M. S Vetrile

N.N. Priorov National Medical Research Center of Traumatology and Orthopaedics

Moscow, Russia

I. N Lisyanskiy

N.N. Priorov National Medical Research Center of Traumatology and Orthopaedics

Moscow, Russia

O. A Polyakova

N.N. Priorov National Medical Research Center of Traumatology and Orthopaedics

Moscow, Russia

V. S Pereverzev

N.N. Priorov National Medical Research Center of Traumatology and Orthopaedics

Moscow, Russia

S. N Makarov

N.N. Priorov National Medical Research Center of Traumatology and Orthopaedics

Moscow, Russia

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