Surgical Treatment for Severe Decompensated Neuromuscular Scoliosis in Patient with Spinal Muscular Atrophy type II

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Treatment results for 16 years old patient with grade 4 thoracolumbar scoliosis on the background of Type II spinal muscular atrophy are presented. One step surgical treatment via dorsal approach was performed: posterior corrective two-rodtranspedicular corporal screw C7 - S1 fusion with fixationof iliac bones by transpedicular system with bone autoplasty + osteomatrix. Surgical intervention resulted in the formation of satisfactory trunk balance, reduction of pelvic distortion and improvement of the patient’s quality of life.

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About the authors

A. N Baklanov

Medicina Clinic Spine Pathology Center

Moscow, Russia

A. N Shaboldin

Medicina Clinic Spine Pathology Center

Moscow, Russia

B. Yu Barchenko

Medicina Clinic Spine Pathology Center

Moscow, Russia


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