Surgical Treatment of Severe Spine Deformity in Patients with Spinal Muscular Atrophy

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Abstract

Two-step surgical treatment was conducted in a 17 year old woman with extremely severe kyphoscoliotic deformity on the background of spinal muscular atrophy. At first step a ring of haloapparatus was assembled and gradual halotraction was performed in an armchair within 21 days. Second step included dorsal correction and stabilization of scoliosis by hybrid fixation system at Th3-L4 level with pelvis fixation. As a result of surgical intervention a proper trunk balance was formed, pelvic deformity was diminished, selfservice and use of wheelchair in a sitting position was improved.

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Хирургическое лечение тяжелой деформации позвоночника у пациентки со спинальной мышечной атрофией
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References

  1. Козлова С.И., Демикова Н.С. Наследственные синдромы и медико-генетическое консультирование. М.: КМК, Авторская академия; 2007: 174–5.
  2. Baumbach Reardon L, Sacharow S, Ahearn M.E. Spinal Muscular Atrophy, X-Linked Infantile. Seattle (WA): University of Washington, Seattle; 1993.
  3. Barsdorf A.I., Sproule D.M., Kaufmann P. Scoliosis surgery in children with neuromuscular disease: findings from the US National Inpatient Sample, 1997 to 2003. Arch. Neurol. 2010; 67 (2): 231–5.
  4. Fujak A., Kopschina C., Gras F., Forst R., Forst J. Contractures of the lower extremities in spinal muscular atrophy type II. Descriptive clinical study with retrospective data collection. Ortop. Traumatol. Rehabil. 2011; 13 (1): 27–36.
  5. Fujak A., Kopschina C., Forst R., Mueller L.A., Forst J. Use of orthoses and orthopaedic technical devices in proximal spinal muscular atrophy. Results of survey in 194 SMA patients. Disabil. Rehabil. Assist. Technol. 2011; 6 (4): 305–11.
  6. Brown J., Zeller J., Swank S., Furumasu J., Warath S.L. Surgical and functional results of spine fusion in spinal muscular atrophy. Spine. 1989; 14 (7): 763–70.
  7. Fujak A., Raab W., Schuh A., Kreb A., Forst R., Forst J. Operative treatment of scoliosis in proximal spinal muscular atrophy: results of 41 patients. Arch. Orthop Trauma Surg. 2012; 132 (12): 1697–706.
  8. Master D.L., Son Hing J.P., Poe Kochert C., Armstrong D.G., Thompson G.H. Risk factors for major neuromuscular scoliosis. Spine. 2011; 7: 564–571.
  9. Исаков Ю.Ф., Степанов Э.А., Красовская Т.В. Абдоминальная хирургия у детей: Руководство АМН СССР. М.: Медицина; 1988: 59–81.
  10. Phillips J.H., Knapp D.R. Jr, Herrera Soto J. Mortality and morbidity in early- onset scoliosis surgery. Spine (Phila Pa 1976). 2013; 38 (4): 324–7.
  11. Bell D., Moseley C., Koreska J. Unit rod segmental spinal instrumentation in the management of patients with progressive neuromuscular spinal deformity. Spine. 1988; 14: 1301–7.
  12. Brown C.A., Lenke L.G., Bridwell K.H., Geideman W.M., Hasan S.A., Blanke K. Complications of pediatric thoracolumbar and lumbar pedicle screws. Spine. 1998; 23 (14): 1566–71.
  13. Broom M.J., Banta J.V., Renshaw T.S. Spinal fusion augmented by Luque-rod segmental instrumentation for neuromuscular scoliosis. J. Bone Joint Surg. Am. 1989; 71 (1): 32–44.
  14. Greggi T., Lolli F., Di Silvestre M., Martikos K., Vomma ro F., Maredi E., Giacomini S., Baioni A., Cioni A. Surgical treatment of neuromuscular scoliosis: current techniques. Stud. Health Technol. Inform. 2012; 176: 315–8.
  15. Modi H.N., Suh S.W., Hong J.Y., Cho J.W., Park J.H., Yang J.H. Treatment and complications in flaccid n e u r o m u s c u l a r s c o l i o s i s (Duchenne muscular dystrophy and spinal muscular atrophy) with posterior-only pedicle screw instrumentation. Eur. Spine J. 2010; 19 (3): 384–93.
  16. Piazzolla A., Solarino G., De Giorgi S., Mori C.M., Moretti L., De Giorgi G. Cotrel-Dubousset instrumentation in neuromuscular scoliosis. Eur. Spine J. 2011; 20 Suppl 1: S75–84.
  17. Mangone M., Raimondi P., Paoloni M., Pellanera S., Di Michele A., Di Renzo S., Vanadia M., Dimaggio M., Murgia M., Santilli V. Vertebral rotation in adolescent idiopathic scoliosis calculated by radiograph and back surface analysis-based methods: correlation between the Raimondi method and rasterstereography. Eur. Spine J. 2013; 22 (2): 367–71.

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