Hip Subluxation in a Patient with Charcot-Marie- Tooth Disease and Osteo-Onychodysplasia


Clinical observation of an 8 years old patient with hip joints instability against the background of two genetic syndromes - Charcot-Marie-Tooth motor and sensory neuropathy and osteo-onychodysplasia is presented. Peculiarities of clinical, roentgenologic, neurologic picture, diagnosis and approaches to the treatment are described. Thorough examination enabled to develop the individual treatment plan and prevent neurologic complications.

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About the authors

I. Yu Pozdnikin

Turner Scientific and Research Institute for Children’s Orthopedics

Email: pozdnikin@gmail.com

M. M Kamosko

Turner Scientific and Research Institute for Children’s Orthopedics

D. B Barsukov

Turner Scientific and Research Institute for Children’s Orthopedics

O. V Barlova

Turner Scientific and Research Institute for Children’s Orthopedics


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